Effect of dystrophin gene deletions on mRNA levels and processing in Duchenne and Becker muscular dystrophies, Cell, vol.63, issue.6, pp.1239-1248, 1990. ,
DOI : 10.1016/0092-8674(90)90419-F
Scoliosis in patients with Duchenne muscular dystrophy, J Bone Joint Surg Am. févr, vol.89, issue.1, pp.155-162, 2007. ,
Respiratory problems in severe scoliosis], Bull Académie Natl Médecine, vol.183, issue.4, pp.721-730, 1999. ,
Respiratory muscle decline in duchenne muscular dystrophy, Pediatric Pulmonology, vol.40, issue.5, 2013. ,
DOI : 10.1183/09031936.00161011
Effect of spinal surgery on lung function in Duchenne muscular dystrophy., Thorax, vol.50, issue.11, pp.1173-1178, 1995. ,
DOI : 10.1136/thx.50.11.1173
Posterior Spinal Fusion for Scoliosis in Duchenne Muscular Dystrophy Diminishes the Rate of Respiratory Decline, Spine, vol.32, issue.4, pp.459-465, 2007. ,
DOI : 10.1097/01.brs.0000255062.94744.52
The Natural History of Cardiac and Pulmonary Function Decline in Patients With Duchenne Muscular Dystrophy, Spine, vol.36, issue.15, pp.1009-1017, 2011. ,
DOI : 10.1097/BRS.0b013e3181fea1ed
Phenotypic heterogeneity of Duchenne myopathy and prognosis criteria]. Arch Pédiatrie Organe Off Sociéte Fr Pédiatrie, juin, vol.16, issue.6, pp.681-683, 2009. ,
Longitudinal Study of Spinal Deformity in Duchenne Muscular Dystrophy, Journal of Pediatric Orthopaedics, vol.13, issue.4, pp.478-488, 1993. ,
DOI : 10.1097/01241398-199307000-00012
[A unique theory on the course of scoliosis, Presse Médicale. 23 mai, pp.1141-1146, 1970. ,
A Dutch guideline for the treatment of scoliosis in neuromuscular disorders, Scoliosis, vol.71, issue.Suppl 2, p.14, 2008. ,
DOI : 10.2106/00004623-198971040-00011
Long-term results of spine surgery in Duchenne muscular dystrophy, Neuromuscular Disorders, vol.6, issue.1, pp.61-68, 1996. ,
DOI : 10.1016/0960-8966(95)00019-4
Correlation between Progression of Spinal Deformity and Pulmonary Function in Duchenne Muscular Dystrophy, Journal of Pediatric Orthopaedics, vol.21, issue.1, pp.113-116, 2001. ,
DOI : 10.1097/01241398-200101000-00022
The prognostic value of pre-operative predicted forced vital capacity in corrective spinal surgery for Duchenne's muscular dystrophy, Anaesthesia, vol.14, issue.12, pp.1160-1162, 2004. ,
DOI : 10.1056/NEJM199903253401207
Spinal fusion in patients with Duchenne's muscular dystrophy and a low forced vital capacity. Eur Spine J Off Publ Eur Spine Soc Eur Spinal Deform Soc Eur Sect Cerv, Spine Res Soc. oct, vol.12, issue.5, pp.507-512, 2003. ,
Factors of Thoracic Cage Deformity That Affect Pulmonary Function in Adolescent Idiopathic Thoracic Scoliosis, Spine, vol.32, issue.1, pp.106-112, 2007. ,
DOI : 10.1097/01.brs.0000251005.31255.25
Idiopathic scoliosis, The Journal of Bone & Joint Surgery, vol.63, issue.5, pp.702-712, 1981. ,
DOI : 10.2106/00004623-198163050-00003
Methods of Predicting Vital Capacity in Patients with Thoracic Scoliosis, The Journal of Bone & Joint Surgery, vol.52, issue.7, pp.1433-1439, 1970. ,
DOI : 10.2106/00004623-197052070-00017
Pulmonary function in thoracic scoliosis, before and after corrective surgery, Minn Med. août, vol.53, issue.8, pp.839-847, 1970. ,
Correlation of Scoliosis and Pulmonary Function in Duchenne Muscular Dystrophy, Journal of Pediatric Orthopaedics, vol.3, issue.3, pp.347-353, 1983. ,
DOI : 10.1097/01241398-198307000-00014
Lung function in Duchenne muscular dystrophy. Eur Spine J Off Publ Eur Spine Soc Eur Spinal Deform Soc Eur Sect Cerv, Spine Res Soc, vol.4, issue.5, pp.263-267, 1995. ,
Clinical implications of maximal respiratory pressure determinations for individuals with duchenne muscular dystrophy, Archives of Physical Medicine and Rehabilitation, vol.78, issue.1, pp.1-6, 1997. ,
DOI : 10.1016/S0003-9993(97)90001-0
Evaluation of pulmonary function in muscular dystrophy patients requiring spinal surgery, Critical Care Medicine, vol.10, issue.10, pp.645-649, 1982. ,
DOI : 10.1097/00003246-198210000-00005
Scoliosis in Duchenne's muscular dystrophy: a changing trend in surgical management : a historical surgical outcome study comparing sublaminar, hybrid and pedicle screw instrumentation systems. Eur Spine J Off Publ Eur Spine Soc Eur Spinal Deform Soc Eur Sect Cerv, Spine Res Soc. mars, vol.19, issue.3, pp.376-383, 2010. ,
Thoracic scoliosis: exothoracic and endothoracic deformations and the spinal penetration index], Rev Chir Orthopédique Réparatrice Appar Mot. févr, vol.88, issue.1, pp.9-18, 2002. ,
Spinal penetration index: new three-dimensional quantified reference for lordoscoliosis and other spinal deformities, Journal of Orthopaedic Science, vol.8, issue.1 ,
DOI : 10.1007/s007760300007
Pathologies neuromusculaires??: imagerie des complications thoraciques, digestives et urinaires, Journal de Radiologie, vol.91, issue.12, pp.1419-1436, 2010. ,
DOI : 10.1016/S0221-0363(10)70221-3
Lung Function Accurately Predicts Hypercapnia in Patients With Duchenne Muscular Dystrophy, Chest, vol.131, issue.2, pp.368-375, 2007. ,
DOI : 10.1378/chest.06-1265
Long??term noninvasive ventilation in children and adolescents with neuromuscular disorders, European Respiratory Journal, vol.22, issue.4, pp.631-636, 2003. ,
DOI : 10.1183/09031936.03.00044303a
Diagnosis and management of Duchenne muscular dystrophy, part 1: diagnosis, and pharmacological and psychosocial management, The Lancet Neurology, vol.9, issue.1, pp.77-93, 2010. ,
DOI : 10.1016/S1474-4422(09)70271-6
Effect of thoracic bracing on lung function in children with neuromuscular disease]. Ann Réadapt Médecine Phys Rev Sci Société Fr Rééduc Fonct Réadapt Médecine Phys, nov, vol.50, issue.8, pp.645-650, 2007. ,
Diagnosis and management of Duchenne muscular dystrophy, part 2: implementation of multidisciplinary care, The Lancet Neurology, vol.9, issue.2, pp.177-189, 2010. ,
DOI : 10.1016/S1474-4422(09)70272-8
histoire naturelle et corrélations des paramètres respiratoires et moteurs dans la dystrophie musculaire de Duchenne, 2012. ,
Duchenne Muscular Dystrophy: Continuous Noninvasive Ventilatory Support Prolongs Survival, Respiratory Care, vol.56, issue.6, pp.744-750, 2011. ,
DOI : 10.4187/respcare.00831
Non-invasive mechanical ventilation: when to start for what benefit?, Thorax, vol.60, issue.12, pp.979-980, 2005. ,
DOI : 10.1136/thx.2005.040394
Nocturnal hypoxaemia and hypercapnia in children with neuromuscular disorders, European Respiratory Journal, vol.39, issue.5, pp.1206-1212, 2012. ,
DOI : 10.1183/09031936.00087511
Early corticosteroid treatment in 4 duchenne muscular dystrophy patients: 14-year follow-up, Muscle & Nerve, vol.20, issue.Suppl 1, pp.796-802, 2012. ,
DOI : 10.1016/j.nmd.2010.07.193
Respiratory surveillance of patients with Duchenne and Becker muscular dystrophy, J Pediatr Rehabil Med, vol.2, issue.2, pp.115-122, 2009. ,
Pulmonary Function and Scoliosis in Duchenne Dystrophy, Journal of Pediatric Orthopaedics, vol.8, issue.2, pp.133-137, 1988. ,
DOI : 10.1097/01241398-198803000-00002
Perioperative respiratory management of pediatric patients with neuromuscular disease, Pediatric Anesthesia, vol.18, issue.Suppl. 1, pp.770-776, 2013. ,
DOI : 10.1177/08830738030180011201
Cardiac and Pulmonary Function Variability in Duchenne/Becker Muscular Dystrophy: An Initial Report, Journal of Child Neurology, vol.74, issue.9, pp.1110-1115, 2010. ,
DOI : 10.1371/journal.pone.0004347
Spirometry is Affected by Intelligence and Behavior in Duchenne Muscular Dystrophy, Pediatric Pulmonology, vol.6, issue.5, pp.408-413, 2005. ,
DOI : 10.1212/WNL.39.4.475
Respiratory Muscle Testing, American Journal of Respiratory and Critical Care Medicine, vol.174, issue.1, pp.67-74, 2006. ,
DOI : 10.1136/thx.35.8.603
The effect of spine fusion on respiratory function in Duchenne muscular dystrophy, Neurology, vol.41, issue.1, pp.38-40, 1991. ,
DOI : 10.1212/WNL.41.1.38
Ventilatory parameters and maximal respiratory pressure changes with age in Duchenne muscular dystrophy patients, Pediatric Pulmonology, vol.136, issue.6, pp.552-559, 2010. ,
DOI : 10.1164/ajrccm/136.4.829
Sniff nasal inspiratory pressure: what is the optimal number of sniffs?, European Respiratory Journal, vol.27, issue.5, pp.980-982, 2006. ,
DOI : 10.1183/09031936.06.00121305
Sniff nasal inspiratory pressure in children with muscular, chest wall or lung disease, European Respiratory Journal, vol.33, issue.1, pp.113-117, 2009. ,
DOI : 10.1183/09031936.00050708
Measuring inspiratory muscle strength in neuromuscular disease: one test or two?, European Respiratory Journal, vol.31, issue.1, pp.93-98, 2008. ,
DOI : 10.1183/09031936.00094707