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DCC) est une maladie constitutionnelle de l'os, associant un retard de fermeture des fontanelles du crâne, des clavicules aplasiques ou hypoplasiques et entrainant entre autres, des anomalies de la dentiton ,
nous aborderons les différentes thérapeutiques envisageables pour traiter les anomalies dento-maxillaires. Dans une quatrième partie nous étudierons un cas familial ,